mohammad hallaj moghadam; Seyed Reza Habibzadeh Shojaei Habibzadeh Shojaei
Abstract
Ehlers Danlos syndrome (EDS) is an inherited connective tissue disease due to impaired collagen metabolism. Joint hypermobility and skin hyper extensibility are the major findings. Six types of EDS are recognized. Type I or Gravis type is characterized by skin hyperextensibility, joint hypermobility, ...
Read More
Ehlers Danlos syndrome (EDS) is an inherited connective tissue disease due to impaired collagen metabolism. Joint hypermobility and skin hyper extensibility are the major findings. Six types of EDS are recognized. Type I or Gravis type is characterized by skin hyperextensibility, joint hypermobility, skin splitting autosoml dominancy inheritance, preterm premature rupture of membrane (PPROM) and varicose vein. Mental retardation has not been reported in the literature. Two cases of unusual type 1 EDS with joint deformity and mental retardation will be reported in this article.
Mohammad Hallaj moghadam; Ali Parsa; Seyed Reza Habibzadeh Shojaei
Abstract
Congenital convex pes valgus or congenital veBackground: The most common method of treatment for vertical talus is the extensive soft tissue release. A minimally-invasive method based on Dobb's serial casting (Reverse Ponseti) was introduced 15 years ago and has yielded significant results. The aim of ...
Read More
Congenital convex pes valgus or congenital veBackground: The most common method of treatment for vertical talus is the extensive soft tissue release. A minimally-invasive method based on Dobb's serial casting (Reverse Ponseti) was introduced 15 years ago and has yielded significant results. The aim of this study was to investigate and compares the midterm results of Casting with the extensive soft tissue release method.Methods:12 patients with vertical talus were included in a prospective study, 6 patients with 10 feet were treated with reverse ponseti, and 6 other patients with 10 feet with externsive soft tissue release. In an 18-24 months follow-up the results were compared together, using ankle range of motion, oxford questionnaire, and radiographic measurements.Results: The mean range of ankle motion was comparable in the two groups (p=0.35), the oxford questionnaire score was not statistically different between the two groups (p=0.876).Conclusion: With the comparable results between the ''reverse-ponseti'' casting land extensive surgical releases in this mid-term study, the casting technique is recommended because of its lower cost and non-invasive nature.rtical talus (CVT) is an uncommon congenital foot deformity. Incidence rate of CVT is 1 out of 10,000 live birth. CVT is one of the main causes of rigid flatfoot in newborns (1). Rigid talonavicular joint dislocation is the hallmark (inflexible in the sole of the foot with no arch) of CVT, accompanied by non-flexible equinus. In this structural abnormality, in fact, the convex plantar surface of the foot creates a rocker-bottom appearance (2). It occurs as an isolated deformity in half of patients and is associated with neuromuscular and genetic disorders in others (1, 3, 4). There is bilateral involvement in half of CVT patients, and there is no gender predilection (5). Although CVT is not painful for newborns and infants, if not diagnosed and left untreated, leads to major disabilities in the adulthood. Ambulation is not usually delayed; however, the gait is unbalanced. Patient`s shoes often show abnormal wear, and pain often develops in early adolescence (6). As the heels, do not touch the ground, push-off from the floor is poor and talar head acts as a weight-bearing structure, resulting in painful calluses in this region (7, 8).
